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HEMANGIOBLASTOMA VON HIPPEL LINDAU DISEASE VHL
Hemangioblastoma Von Hippel Lindau Disease VHL
Hemangioblastoma Von Hippel Lindau Disease VHL: Hemangioblastomas are central nervous system tumors that originate from the vascular system usually during middle age. Sometimes these tumors also appear elsewhere in the central nervous system, such as the spinal cord and the retina. Hemangioblastoma central nervous system tumors can be associated with other diseases such as polycythaemia (increased number of blood cells), pancreatic cysts, in which cases we have Von Hippel-Lindau syndrome.
Haemangioblastomas most often consist of stromal cells in small blood vessels and are usually found in the cerebellum, brain stem or spinal cord.
The primary diagnosis is done with CT scan. Magnetic tomography is essential for surgical planning for Hemangioblastoma Von Hippel Lindau Disease VHL.
Treatment: Hemangioblastoma Von Hippel Lindau Disease VHL
Treatment for hemangioblastoma is surgical removal of the tumor.
The prognosis for single hemangioblastoma is very good if radical resection of the tumor can be achieved. This is possible if the diagnosis is timely, and the tumor is treated with all modern microsurgical techniques. In people with Von Hippel-Lindau syndrome, the prognosis is worse as the tumors are usually multiple and radical surgery is difficult.